Familial Hypertrophic Cardiomyopathy

  • Praveen Kerala Varma Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
  • Narayanan Namboodiri Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
DOI: https://doi.org/10.52314/kmj.2019.v12i1.553
Keywords: Hypertrophic Cardiomyopathy, Systolic Anterior Motion, Left ventricular outflow obstruction, Heart Failure, Mitral Regurgitation

Abstract

Hypertrophic Cardiomyopathy is the most common genetic cardiovascular disease. 70% of affected individuals demonstrate resting or provoked obstruction across the left ventricle (LV) outflow tract. Pathophysiology and clinical course are determined by the hypertrophy of LV. dynamic and mechanical left ventricular outflow tract occlusion, mitral regurgitation, diastolic dysfunction and myocardial ischemia, fibrosis, ventricular tachycardia and risk of sudden death. Patients are initially managed medically, however, significant heart failure symptoms or syncope in spite of optimal drug therapy and significant obstruction require invasive therapy. We report a case of familial hypertrophic cardiomyopathy treated successfully by surgical myectomy.

Author Biographies

Praveen Kerala Varma, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India

Additional Professor, Senior resident, Division of Cardiac surgery

Narayanan Namboodiri, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India

 Associate Professor, Division of Cardiology and Electrophysiology

Published
2019-03-25
How to Cite
Varma, P., & Namboodiri, N. (2019). Familial Hypertrophic Cardiomyopathy. Kerala Medical Journal, 12(1), 24-26. https://doi.org/10.52314/kmj.2019.v12i1.553
Issue
Vol 12 No 1 (2019): January to March 2019
Section
Case Series / Case Report

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